Pierre Robin syndrome factsheet


Pierre Robin Syndrome is a congenital condition characterised by: 

  • small lower underdeveoloped jaw (micrognathia)
  • cleft palate (when a baby is born with an opening (a cleft) in the roof of the mouth, leaving a hole between the nose and the mouth)
  • displacement of the tongue towards the back of the throat (glossoptosis). 

Sometimes the condition can be so severe that a breathing tube may need to be placed to support the child’s breathing. 

 Signs and symptoms

Babies born with Pierre Robin syndrome commonly experience trouble breathing and feeding early on, because of the tongue’s position, smaller jaw size and the cleft palate formation.

Additional symptoms of Pierre Robin may  include:

  • snoring and airway obstruction due to displacement of tongue at the back of the throat
  • repeated ear infections or temporary hearing loss 
  • natal teeth (teeth that are present at birth). 


Your healthcare provider can diagnose Pierre Robin syndrome with a physical examination.

Genetic testing can also help rule out other related health issues.


If your child has Pierre Robin syndrome, you can expect treatment to come in stages. 

Since the condition affects a variety of functions, including hearing, breathing and feeding, several specialists will be involved in your child’s care.


The first priority will be to keep the upper airway open to allow for proper breathing. Laying your child on his or her stomach can help prevent the tongue from blocking off the airway. 

Other treatments aimed at keeping the upper airway open may be recommended. These include a nasopharyngeal airway or nasal trumpet (a small tube threaded through the nose into the upper airway).

In cases of severe obstruction, your doctor may recommend surgery to enlarge the lower jaw (so that the tongue can come into the mouth) or a tracheotomy to create an opening in the windpipe.

Cleft palate

The timing of the cleft palate repair varies depending on the child’s individual growth and development. It is typically addressed within 1 to 2 years of age.

Cleft palate is repaired with a two- to three-hour surgical procedure and requires a one- to two-night hospital stay. During the procedure, tubes may be inserted into the ear to lessen fluid buildup.

Some children may also require speech therapy following cleft palate repair.


Management of Pierre Robin Syndrome is a team-based apporach  between craniofacial surgeons, intensivists, ENT surgeons and speech therapists. Some children require elongation of their jaws in the first months of life. 

Parents and doctors should continue to monitor child development — particularly jaw and tooth development, growth, and speech — after treatment for conditions related to Pierre Robin syndrome.


If your baby has been diagnosed with Pierre Robin syndrome, special care and attention must be given during feeding times to prevent liquids from going into the airway. In some cases, your healthcare provider may recommend a feeding tube to avoid choking.

While feeding difficulties decrease within the first two years, children that may need long-term assistance could require a gastric tube inserted into the abdominal wall.

Teeth problems

Since the lower jaw is smaller in children with Pierre Robin sequence, teeth crowding is frequently a concern. Orthodontists, paediatric dentists and craniofacial surgeons should work together to monitor dental development.

Resources and more information

Healthdirect provides free, trusted health information and advice, 24 hours a day, 7 days a week online or via telephone 1800 022 022. 

Last updated Wednesday 8th May 2024


This factsheet is provided for general information only. It does not constitute health advice and should not be used to diagnose or treat any health condition.

Please consult with your doctor or other health professional to make sure this information is right for you and/or your child.

The Sydney Children’s Hospitals Network does not accept responsibility for inaccuracies or omissions, the interpretation of the information, or for success or appropriateness of any treatment described in the factsheet.

© Sydney Children’s Hospitals Network 2024

This factsheet was produced with support from John Hunter Children's Hospital.